Β | Heterotaxy (%) | Non-heterotaxy (%) | P value |
---|---|---|---|
N | 39 | 71 | Β |
Observation period (mo) | 90.8βΒ±β93.9 | 107.7βΒ±β56.1 | 0.310 |
Male | 25 (64.1) | 35 (49.3) | 0.163 |
Major associated anomaly | |||
Pulmonary atresia | 19 (48.7) | 23 (32.4) | 0.344 |
Anomalous pulmonary venous return | 14 (35.9) | 6 (8.5) | 0.079 |
Age of 1st palliation (mo) | 3.0βΒ±β3.1 | 2.9βΒ±β6.7 | 0.907 |
1st palliation | Β | Β | 0.546 |
BT shunt | 25 (64.1) | 46 (64.8) | Β |
PAB | 2 (5.1) | 10 (14.1) | Β |
BCPS | 12 (30.8) | 15 (21.1) | Β |
Mortality | 16 (41.0) | 8 (11.3) | 0.001 |
Median age of death (range) (mo) | 4.4 (1.2-221.1) | 9.4 (3.1-35.7) | 0.427 |
Median time to death after palliation (range) (mo) | 2.5 (0.6-62.2) | 5.1 (1.7-32.3) | 0.838 |
Causes of death | |||
Infection | 6 (37.5) | 3 (37.5) | Β |
Sudden death | 5 (31.3) | 3 (37.5) | Β |
Arrhythmia | 2 (12.5) | 0 | Β |
Pulmonary venous obstruction | 2 (12.5) | 1 (12.5) | Β |
Heart failure | 1 (6.3) | 1 (12.5) | Β |
Time of mortality | Β | Β | 0.722 |
Before BCPS | 13 (81.3) | 6 (75.0) | Β |
After BCPS | 3 (18.7) | 2 (25.0) | Β |