Skip to main content

Table 1 Differences between heterotaxy and non-heterotaxy patients

From: Interstage mortality for functional single ventricle with heterotaxy syndrome: a retrospective study of the clinical experience of a single tertiary center

  Heterotaxy (%) Non-heterotaxy (%) P value
N 39 71  
Observation period (mo) 90.8 ± 93.9 107.7 ± 56.1 0.310
Male 25 (64.1) 35 (49.3) 0.163
Major associated anomaly
Pulmonary atresia 19 (48.7) 23 (32.4) 0.344
Anomalous pulmonary venous return 14 (35.9) 6 (8.5) 0.079
Age of 1st palliation (mo) 3.0 ± 3.1 2.9 ± 6.7 0.907
1st palliation    0.546
BT shunt 25 (64.1) 46 (64.8)  
PAB 2 (5.1) 10 (14.1)  
BCPS 12 (30.8) 15 (21.1)  
Mortality 16 (41.0) 8 (11.3) 0.001
Median age of death (range) (mo) 4.4 (1.2-221.1) 9.4 (3.1-35.7) 0.427
Median time to death after palliation (range) (mo) 2.5 (0.6-62.2) 5.1 (1.7-32.3) 0.838
Causes of death
Infection 6 (37.5) 3 (37.5)  
Sudden death 5 (31.3) 3 (37.5)  
Arrhythmia 2 (12.5) 0  
Pulmonary venous obstruction 2 (12.5) 1 (12.5)  
Heart failure 1 (6.3) 1 (12.5)  
Time of mortality    0.722
Before BCPS 13 (81.3) 6 (75.0)  
After BCPS 3 (18.7) 2 (25.0)  
  1. BT Blalock-Taussig, PAB pulmonary artery banding, BCPS bidirectional cavo-pulmonary shunt.