Atrial switch n = 20 | ASO n = 12 | Nikaidoh n = 7 | Rastelli n = 48 | REV n = 24 | |
---|---|---|---|---|---|
Male | 14 (70%) | 10 (71%) | 5 (71%) | 25/48 (52%) | 13 (54%) |
Age (years) | 1.2 (0.8–3.9) | 0.3 (0.1–4.1) | 3.4 (2.3–3.9) | 5.3 (4.3–8.0) | 3.8 (2.3–6.2) |
Body weight (kg) | 7.5 (5.7–12.6) | 4.3 (3.5–12.8) | 11.7 (10.3–12.3) | 16.7 (13.4–21.4) | 14.5 (10.1–16.1) |
Type of LVOT obstruction Valvular Subvalvular Valvular and subvalvular Atresia | 5 (25%) 13 (65%) 2 (10) None | 1 (8%) 9 (75%) 2 (17%) None | 5 (71%) 2 (29%) None None | 16 (33%) 3 (6%) 17 (35%) 12 (25%) | 7 (29%) 3 (13%) 11 (46%) 3 (13%) |
Type of ventricular septal defect Intact septum Infundibular Perimembranous Muscular Multi-level | 9 (50%) 1 (6%) 10 (50%) None None | 1 (8%) 6 (50%) 3 (21%) 1 (8%) 1 (8%) | None 1 (14%) 6 (86%) None None | None 4 (8%) 38 (79%) None 6 (13%) | None 6 (25%) 14 (58%) None 4 (17%) |
Bicuspid pulmonary valve | 6 (30%) | 2 (17%) | 3 (43%) | 8 (17%) | 4 (17%) |
Z-score of pulmonary diameter in valvular LVOTO | − 0.20 (− 0.21–0.19) | 0.73 (0.63–0.87) | − 0.64 (− 0.45–− 0.91) | − 3.84 (− 4.82–− 3.43) | − 1.99 (− 2.74–− 0.35) |
Pulmonary/aorta ratio in valvular LVOTO | 0.83 ± 0.07 | 1.06 ± 0.05 | 0.65 ± 0.09 | 0.54 ± 0.13 | 0.71 ± 0.24 |
Fractional shortening | 0.34 ± 0.09 | 0.38 ± 0.08 | 0.42 ± 0.04 | 0.37 ± 0.07 | 0.37 ± 0.06 |
Pressure gradient in LVOT (mmHg) | 45 (30–56) | 40 (27–63) | 57.5 (35.8–66.5) | 65 (58–79) | 65 (47–73) |