Volume 10 Supplement 1

Proceedings of the WSCTS 25th Anniversary Congress

Open Access

Surgical treatment of congenital anomalies of the aortic arch : Long-term results

  • Fabio Cuttone1,
  • Romain Amadieu2,
  • Géraldine Labouret3,
  • Lionel Berthomieu4,
  • Sophie Breinig4,
  • Sebastien Hascoet2,
  • Khaled Hadeed2,
  • Daniel Roux1,
  • Yves Dulac2,
  • Philippe Acar2 and
  • Bertrand Leobon1
Journal of Cardiothoracic Surgery201510(Suppl 1):A66

https://doi.org/10.1186/1749-8090-10-S1-A66

Published: 16 December 2015

Background/Introduction

Congenital anomalies of the aortic arch gather a wide spectrum of malformations concerning the aortic arch or some of its branches and the pulmonary artery. These malformations are rare (1 in 1000 live births) and sometimes responsible of complete (vascular ring) or partial (vascular sling) encirclement of the oesophagus, trachea or bronchi. In cases of symptomatic airways obstruction or oesophagus compression the surgical treatment is mandatory and curative.

In this paper we describe the experience of Children's Hospital of Toulouse on the surgical treatment of congenital anomalies of aortic arch.

Aims/Objectives

To evaluate the results and the clinical outcome of reconstructive surgery in patients affected by symptomatic vascular ring.

Method

Observational retrospective monocentric study including all the patients with a congenital anomaly of the aortic arch submitted to surgical treatment since May 2010, at the Children's Hospital of Toulouse.

Results

Between May 2010 and March 2015, 10 patients (3 girls and 8 boys) underwent surgical treatment for vascular ring responsible for a tracheo-esophageal compression: 9 double aortic arch including 7 right dominant arches, 1 left dominant, 1 balanced disposition and 1 child with a Neuhauser anomaly.

The average age and weight were respectively 2.5 ± 1.5 years and 12.9 ± 3.7 kg. Surgical correction was carried out mainly by postero-lateral thoracotomy and was performed without complication. The mean duration of mechanical ventilation was 6 ± 7 hours and the average length of stay in intensive care was 1.7 ± 0.7 days. The average hospital stay was 4.8 ± 1.2 days. All patients are alive at the time of the last follow-up and asymptomatic with normal growth.

Discussion/Conclusion

In this series, the surgical treatment of aortic arch anomalies was curative in all cases without associated morbidity and with good functional midterm results. The diagnosis is often delayed and more frequently suspected on the basis of respiratory symptoms.

Consent

Written informed consent was obtained from the patient for publication of this abstract and any accompanying images. A copy of the written consent is available for review by the Editor of this journal.

Authors’ Affiliations

(1)
Department of Cardiac Surgery, University Hospital (CHU)
(2)
Department of Cardiology, University Hospital (CHU)
(3)
Department of Pediatric Pneumology and Allergology, University Hospital (CHU)
(4)
Department of Pediatric Intensive Care Unit, University Hospital (CHU)

Copyright

© Cuttone et al. 2015

This article is published under license to BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.

Advertisement