Male/Female (case)
|
18(72%)/7(28%)
|
Age(year)
|
44 ± 15.7(16~70)
|
Duration (weeks)
|
26 ± 51.0(0.83~216)
|
Pneumothorax type (case)
| |
Pneumothorax
|
11(44%)
|
hydropneumothorax
|
5 (20)
|
empyemaa
|
8 (32%)
|
Hemopneumothorax
|
1 (4%)
|
Chest Imaging(n)
| |
Nodules (Multi/Single)
|
22(88%)
|
Cavity
|
21(84%)
|
Pulmonary hemorrhage
|
1 (4%)
|
Extrapulmonary manifestations (n)
| |
Fever
|
11(44%)
|
Skin lesions (purpura, gangrene, ulcers, etc.)
|
7 (28%)
|
Nasal and sinus involvement
|
15(60%)
|
Oral ulcers
|
5 (20%)
|
Glomerulonephritis and other
|
13(52%)
|
Nervous system (facial paralysis, mononeuropathy, etc.)
|
6 (24%)
|
Arthralgia/arthritis
|
11(44%)
|
Parotid swelling
|
2 (8%)
|
Laboratory tests
| |
ANCA-positive(n)
|
13/20(65%)
|
Anti-PR3(RU/ml)
|
176 ± 145.3(26~411)
|
ESR (mm/h)
|
92 ± 31.6(24~145)
|
CRP (mg/dl)
|
20 ± 27.4(2.35–90)
|
Pleural drainage(n)
|
16
|
Surgery(n)
|
7 (28%)
|
Spontaneous absorption(n)
|
4 (16%)
|
Death
|
10(40%)
|