Table 1 ALCAPA syndrome diagnosed in children and adolescents: patient demographics, clinical, imaging data and outcome data

Gender

F

M

M

M

F

F

M

M

M

Age

15

13

5

14

7

5

6

16

5

Presenting symptoms

NO

NO

NO

syncope

NO

No

No

No

No

NYHA Class

I

II

I

I

I

I

I

I

I

Heart Murmur

Yes

Yes

Yes

Yes

Yes

Yes

Yes

Yes

Yes

Abnormal ECG

Yes

–

No

Yes

Yes

Yes

Yes

Yes

Yes

Abnormal CXR

Yes

Yes

Yes

–

Yes

Yes

Yes

No

Yes

MR grade at diagnosis

mild

No

No

mild

severe

severe

moderate

moderate

No

LVEF%

66

64

68

66

65

59

63

70

70

Preoperative arrhythmia

No

No

No

No

No

No

No

No

No

Type of ALCAPA surgery

Takeuchi/VSD closure

N/A

reimplantation

Takeuchi

reimplantation/Mitral repair

reimplantation/Mitral repair

reimplantation

Takeuchi

reimplantation

Follow up to date (years)

7

–

0.5

0.5

3

1

1

2

1

Postoperative arrhythmia

No

–

–

No

No

No

No

No

No

Device implantation

No

–

No

No

No

No

No

Yes

No

CPB Time (min)

145

–

145

150

171

175

76

118

146

Aortic Occlusion Time (min)

103

–

103

116

138

128

45

91

117

Transfusion

Yes

–

Yes

Yes

Yes

Yes

Yes

Yes

Yes