Pleomorphic adenoma is the most common tumor of the major salivary glands, usually developing in the palate, tongue, nasopharynx or larynx. Its primary location in the lungs is extremely rare and it usually arises from the tracheal and bronchial seromucous glands [2, 3]. Pulmonary adenomas usually include bronchial adenoma, alveolar adenoma, papillary adenoma and adenomas of the salivary gland while primary salivary-type lung cancers are rare tumors that include adenoid cystic carcinoma and mucoepidermoid carcinoma. Pleomorphic adenoma constitutes about 1 % of all the cases of primary lung adenomas [2]. Considering age and gender there has not been any proven gender predominance and the patients’ age ranges from 8 to 74 [3], but it seems that they occur more common in younger patients. Clinically, pleomorphic adenoma of the lungs may present with dyspnea and hemoptysis or fever, weight loss, pleural effusion and shortness of breath depending on its location or frequently lacking any symptoms [4], as it occurred in our case. The tumor in our case originated from the right main bronchus according to the thorax CT-scan, which is in lieu with the fact that the pleomorphic adenomas of the lung are commonly centrally positioned. The size of the tumor was 10.6 × 11.1 × 11.6 cm making it one of the biggest pleomorphic adenomas of the lungs considering the literature stating that the size varies from 1.5 to 16 cm in diameter [5] (Fig. 3). Differential diagnosis of primary finding on the X-ray and CT-scan included large interlobular hematoma, echinococcal cyst, hamartoma, and other pulmonary tumors such as blastoma, hamartochondroma and carcinosarcoma. We decided to perform an early surgical procedure because cytological results did not offer a certain response about the nature of the formation. Also, an early surgical procedure was opted for due to the large size and the possibility of a hematoma. Other invasive diagnostic procedures such as endobronchial ultrasound (EBUS) were considered but were not performed after the decision was made about the early surgical procedure. Subsequently, a PET CT was considered preoperatively due to the possibility of the metastasis but since the metastases were described in very few cases it was done postoperatively. The surgical excision is the main treatment for pleomorphic adenoma of the lungs [5]. Although in our case the tumor originated from the right main bronchus, since the pathologist intraoperatively stated that there were no malignant cells present, a sleeve resection and a bronchoplasty were not performed. We decided to wait for the final histopathological diagnosis. If the diagnosis contained findings of malignant cells or unclear resection margins, a more extensive procedure would have been performed in subsequent treatment. Considering the intraoperative histopathology, hilar station lymphadenectomy was deemed sufficient in our case. If the final histopathological diagnosis had indicated so, then we would have performed further mediastinal and aortic lymphadenectomy using video-assisted thoracoscopic surgery (VATS) [6]. The final histopathological diagnosis confirmed it was a pleomorphic adenoma consisting of epithelial elements and tubules with uniform cells and well-shaped round nuclei. Between these cells there was a lot of myxoid stromal and partially chondroid tissue. Considering the size of the tumor in our case video-assisted thoracoscopic surgery (VATS) was not performed, but in cases with smaller tumors VATS is recommended. There have been reported cases of recurrence after surgical excision wherein the metastases where present locally by pleural dissemination or there were distant metastases in the breast and spine [5]. This recurrence may be caused by incomplete excision or due to a core needle biopsy [5, 7].